Osteomas of the nose and paranasal sinus are commonly known as benign neoplasms. Many cases with osteomas show generally asymptomatic findings. On the other hand, some cases with manifest symptoms may require surgical treatment. The most common of these are osteomas in the paranasal sinuses, which can cause recurrent infections and headaches. It has been reported that ethmoid and frontal osteomas could extend to the orbita and cause cosmetic deformity or mucocele formation. Gardner’s syndrome is an autosomal dominant hereditary disorder characterized by clinical triad of intestinal polyposis, osteomas, and cutaneous or soft tissue tumors. Suspected cases of Gardner’s syndrome in patients with paranasal sinus osteomas should have a complete workup for Gardner’s syndrome, including lower gastrointestinal tract endoscopy, barium enema imaging and genetic testing, because early recognition and diagnosis of Gardner’s syndrome will help prevent the development of colon cancer.